Vnitr Lek 2022, 68(4):212-215 | DOI: 10.36290/vnl.2022.045
Antifibrotic therapy and its indications for interstitial pulmonary fibrosis
- Klinika nemocí plicních a TBC Fakultní nemocnice Brno a Lékařské fakulty Masarykovy univerzity Brno
Idiopathic pulmonary fibrosis and chronic fibrotic interstitial lung disease with progressive phenotype are characterized by fibrotic lung parenchyma. Current antifibrotic treatment does not affect pre-existing lung parenchyma fibrosis, but prevents fibrosis progression and reduces mortality by reducing fibrotization. This work summarizes fibrotic lung processes and their treatment options.
Keywords: idiopathic pulmonary fibrosis, progressive fibrosing interstitial lung diseases, nintedanib, pirfenidon.
Published: June 22, 2022 Show citation
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