Vnitr Lek 2009, 55(11):1051-1055

Neuroendocrine tumours of the appendix

O. Louthan
Ambulance pro neuroendokrinní nádory IV. interní kliniky 1. lékařské fakulty UK a VFN Praha, přednosta prof. MUDr. Aleš Žák, DrSc.

According to WHO, neuroendocrine tumors of the appendix (appendiceal carcinoids) are defined as 1. well-differentiated endocrine tumors with benign or uncertain behavior, 2. well-differentiated endocrine carcinoma and 3. goblet cell carcinoma. These tumors are usually diagnosed incidentally during appendectomy. Carcinoid syndrome is rare in appendiceal carcinoid. Tumor size greater than 2 cm is the most important parameter for prognosis. Most patients are cured by appendectomy (appendiceal tumors ≤ 2 cm), tumors with a diameter > 2 cm should be managed by right hemicolectomy.

Keywords: goblet cell carcinoid; hemicolectomy; neuroendocrine tumor; WHO classification

Received: April 1, 2009; Accepted: April 23, 2009; Published: November 1, 2009  Show citation

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Louthan O. Neuroendocrine tumours of the appendix. Vnitr Lek. 2009;55(11):1051-1055.
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